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Glenn procedure is a palliative surgical procedure performed for patients with Tricuspid atresia.
Tricuspid atresia - a form of congenital heart disease whereby there is a complete absence of the tricuspid valve.
Rare other causes include carcinoid syndrome, endocarditis, endomyocardial fibrosis, lupus erythematosus, right atrial myxoma and congenital tricuspid atresia.
It was initially described in 1971 by Dr Fontan and Dr Kreutzer separately as a surgical treatment for tricuspid atresia.
Such defects include persistent truncus arteriosus, total anomalous pulmonary venous connection, tetralogy of Fallot, transposition of the great vessels, and tricuspid atresia.
Defects in producing the AV septum produces atrioventricular septal defects, including a persistent AV canal and tricuspid atresia.
Malalignment of the septum can cause the congenital heart conditions Tetralogy of Fallot, truncus arteriosus, D-Transposition of the Great Vessels, tricuspid atresia, and TAVPR (Total Anomalous Pulmonary Venous Return).