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IgA pemphigus is a subtype of pemphigus with two distinct forms, subcorneal pustular dermatosis type of IgA pemphigus (distinct from and not to be confused with subcorneal pustular dermatosis) and intraepidermal neutrophilic IgA dermatosis.
Subcorneal pustular dermatosis (also known as "Sneddon-Wilkinson disease") (distinct from and not to be confused with subcorneal pustular dermatosis type of IgA pemphigus) is skin condition that is a rare, chronic, recurrent, pustular eruption characterized histopathologically by subcorneal pustules that contain abundant neutrophils.