nevus flammeus

Nevus flammeus is benign and commonly does not require any treatment.

Facial birth marks (nevus flammeus) appear usually on one side of the face.

Sometimes the term nevus flammeus is divided into two categories: port-wine stain and salmon patch.

Nevus flammeus may be divided as follows:

Children with BWS often have nevus flammeus on their forehead or the back of their neck.

The nevus flammeus type of hemangiomas may not need treatment unless it is disfiguring, psychologically distressing, painful, or it changes in appearance.

Stork bite (Nevus flammeus nuchae)

Port-wine stain (Nevus flammeus)

The three main features are nevus flammeus (port-wine stain), venous and lymphatic malformations, and soft-tissue hypertrophy of the affected limb.

- Vascular anomalies (nevus flammeus /Sturge-Weber/Klippel-Trénauna Adams Oliver syndrome)

A port-wine stain or nevus flammeus is a vascular anomaly consisting of superficial and deep dilated capillaries in the skin that produce a reddish to purplish discoloration of the skin.

Cutaneous lesions described in patients with CMTC include nevus flammeus, hemangioma, nevus anemicus, café-au-lait spots, melanocytic nevus, aplasia cutis and acral cyanosis.

Midline nevus flammeus (also known as "angel's kiss,") is a vascular birthmark which may be found on the glabellar region or on one upper eyelid, and presents in approximately 15% of newborns.

In addition, some children with BWS have other findings including: nevus flammeus, prominent occiput, midface hypoplasia, hemihypertrophy, genitourinary anomalies (enlarged kidneys), cardiac anomalies, musculoskeletal abnormalities, and hearing loss.

Another definition presented by Elliot et al. includes the presence of either three major features (anterior abdominal wall defect, macroglossia, or prepostnatal overgrowth) or two major plus three minor findings (ear pits, nevus flammeus, neonatal hypoglycemia, nephromegaly, or hemihyperplasia).

Angio-Osteohypertrophy Syndrome Congenital Dysplastic Angiectasia Hemangiectatic Hypertrophy Klippel-Trenaunay-Weber Syndrome KTW Syndrome Osteohypertrophic Nevus Flammeus KTS None Klippel-Trenaunay Syndrome, a rare disorder that is present at birth (congenital).