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Both of these diseases result in problems in mucopolysaccharide metabolism.
It is suggested that the mucopolysaccharide deposit could cause strangulation of nerve endings.
Morquio syndrome is an inherited disease belonging to the group of mucopolysaccharide storage diseases.
Despite initial tests not showing increased mucopolysaccharide excretion, the disease was regarded as a mucopolysaccharidosis.
These observations indicated the existence of a new inborn error of the mucopolysaccharide metabolism.
Acemannan is a D-isomer mucopolysaccharide in aloe vera leaves.
Initially there is edema of the connective tissue and increase in acid mucopolysaccharide in the ground substance.
Normal acid mucopolysaccharide values vary with age, and the normal range of values varies among laboratories.
Kakkis, E.D.: Enzyme replacement therapy for the mucopolysaccharide storage disorders.
In both types there is accumulation in the body and brain of abnormally large amounts of a substance called mucopolysaccharide.
Toxicity of an algal mucopolysaccharide for Escherichia coli and Neisseria meningitidis strains.
Gefarnate works by promoting defensive factors such as mucus and acid mucopolysaccharide synthesis in gastric epithelial tissue.
Applying a medicated cream containing mucopolysaccharide polysulfuric acid (e.g., Hirudoid) may also speed the healing process.
It disrupts the structure of acid mucopolysaccharide fibers thereby producing less viscous mucus, which is easier to expectorate.
It has several symptoms in common with other mucopolysaccharide storage diseases such as coarse facial features, short stature, and skeletal and joint abnormalities.
Cells contain a raphe, which allows them to move on surfaces, and an apical porefield, through which a mucopolysaccharide stalk is secreted.
In 1960 Sanfilippo was awarded a postdoctoral research fellowship and began a comprehensive study of children with mucopolysaccharide storage disease at the University of Minnesota.
Moreover, the cornea bears more mucopolysaccharide (a carbohydrate that has among its repeating units a nitrogenous sugar, hexosamine) to embed the fibrils.
This prokaryote produces a rich structured mucopolysaccharide (slime) packaging in the form of interlocking slime funnels.
Dermatan sulfate is a glycosaminoglycan (formerly called a mucopolysaccharide) found mostly in skin, but also in blood vessels, heart valves, tendons, and lungs.
The nature of this material is unknown, but researchers have suggested that it may be a glycoprotein, a glycolipid, an acid mucopolysaccharide, altered collagen or elastic tissue.
Inborn mucopolysaccharide metabolic disorders due to β-glucuronidase deficiency with granular inclusions in granulocytes occurs in the biochemical and metabolic systems.
This disorder is called Pseudo-Hurler because it resembles a mild form of Hurler syndrome, one of the mucopolysaccharide (MPS) diseases.
Sylvester Sanfilippo (January 1, 1926 - May 2, 2013) was a pediatrician from Edina, MN, who first described a mucopolysaccharide storage disease which bears his name.
Morquio's syndrome (referred to as mucopolysaccharidosis IV or Morquio's) is an autosomal recessive mucopolysaccharide storage disease (see also lysosomal storage disorder), usually inherited.