medulloepithelioma

There are few data on which to base treatment of medulloepithelioma and ependymoblastoma tumors.

In newly diagnosed childhood medulloepithelioma and ependymoblastoma, the tumor itself has not been treated.

Treatment of childhood medulloepithelioma or ependymoblastoma in children 3 years old or younger is often within a clinical trial.

Medulloepithelioma of the ciliary body may necessitate enucleation of the eye.

Standard treatment of childhood medulloepithelioma or ependymoblastoma in children 3 years old or younger is usually surgery followed by chemotherapy.

The second most common is medulloepithelioma (also called diktyoma) which can occur in the ciliary body and the uvea of the eye.

Medulloepithelioma.

Both medulloepithelioma and ependymoblastoma are identified as histologically discrete tumors within the WHO classification system.

Histologically, medulloepithelioma resemble a primitive neural tube and with neuronal, glial and mesenchymal elements.

A highly malignant undifferentiated primitive neuroepithelial tumour of children, medulloepithelioma may contain bone, cartilage, skeletal muscle, and tends to metastasize extracranially.

Check for U.S. clinical trials from NCI's list of cancer clinical trials that are now accepting patients with childhood medulloepithelioma.

Medulloepithelioma appears isodense or hypodense with variable heterogeneity and calcification on non-contrast CT scan, and enhances with contrast.

Diktyoma, or ciliary body medulloepithelioma, or teratoneuroma, is a rare tumor arising from primitive medullary epithelium in the ciliary body of the eye.

Medulloepithelioma was originally classified as the most primitive neoplasm of the Central Nervous System (CNS) by Bailey and Cushing in 1926.

Sharma MC, Mahapatra AK, Gaikwad S, et al.: Pigmented medulloepithelioma: report of a case and review of the literature.

Norris LS, Snodgrass S, Miller DC, et al.: Recurrent central nervous system medulloepithelioma: response and outcome following marrow-ablative chemotherapy with stem cell rescue.