It is almost always fatal and usually requires surgical intervention.
It means that we need a new paradigm - something beyond surgical intervention.
Even with early surgical intervention (within 24 hours) the risk of death is 25%.
I'd much rather stay healthy, not need major surgical intervention of any kind.
Other surgical interventions are less urgent and can wait for 1 or 2 years.
Without immediate surgical intervention the patient would not live for more than a few hours.
They may also provide evidence to the doctor whether surgical intervention is necessary.
There's every reason to expect a natural birth; there shouldn't be any need for surgical intervention.
In other words, we don't know how many patients will get better on their own, without any medical or surgical intervention.
There is, however, no evidence for the long-term efficacy of surgical intervention.