hereditary lymphedema

In most cases, hereditary lymphedema is inherited as an autosomal dominant trait.

Hereditary lymphedema is also known as primary lymphedema.

Presented here is an extreme case of severe unilateral hereditary lymphedema which had been present for 25 years without treatment:

Mutations in this gene cause hereditary lymphedema type IA.

It is also known as Milroy disease, Nonne-Milroy-Meige syndrome and hereditary lymphedema.

In hereditary lymphedema, lymphatic fluid collects in the soft tissues in and under the skin (subcutaneous) due to obstruction, malformation, or underdevelopment (hypoplasia) of various lymphatic vessels.

There are three forms of hereditary lymphedema: congenital hereditary lymphedema or Milroy disease; lymphedema praecox or Meige disease; and lymphedema tarda.

Primary Lymphedema Hereditary Lymphedema, Type I Congenital Hereditary Lymphedema Milroy Disease Nonne-Milroy Disease Lymphedema Praecox Lymphedema Tarda Hereditary lymphedema is a genetic developmental disorder affecting the lymphatic system.