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This type of neonatal hepatitis is sometimes called "giant cell hepatitis."
Giant cell hepatitis is a rare form of hepatitis ( 100 cases reported) that predominantly occurs in children.
Infants with giant cell hepatitis usually recover (80 percent of cases) with little or no scarring to their liver.
About 20 percent of the infants with neonatal giant cell hepatitis develop chronic liver disease and cirrhosis.
INH neonatal giant cell hepatitis idiopathic neonatal hepatitis syndrome None Idiopathic neonatal hepatitis is a general term for inflammation of the liver (hepatitis) that occurs shortly after birth in newborns.
Aagenaes syndrome is a syndrome characterised by congenital hypoplasia of lymph vessels, which causes lymphedema of the legs and recurrent cholestasis in infancy, and slow progress to hepatic cirrhosis and giant cell hepatitis with fibrosis of the portal tracts.