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The conus medullaris is situated below the L2 level in more than 75% of these diastematomyelia patients.
The signs and symptoms of diastematomyelia may appear at any time of life, although the diagnosis is usually made in childhood.
Cervical diastematomyelia is a very rare entity.
Adult presentation in diastematomyelia is unusual.
They advised that if the imaging appears to show otherwise, a second spur (present in about 5% of patients with diastematomyelia) is likely to be present.
Lumbosacral adult diastematomyelia is even rarer.
Prenate ultrasound could also detect whether the diastematomyelia is isolated, with the skin intact or association with any serious neural tube defects.
The surgical procedure required for the effective treatment of diastematomyelia includes decompression (surgery) of neural elements and removal of bony spur.
This form of diastematomyelia is not accompanied by any bony spur or fibrous band and is rarely symptomatic unless hydromyelia or tethering is present.
In approximately 60% of patients with diastematomyelia, the two hemicords, each covered by an intact layer of pia arachnoid, travel through a single subarachnoid space surrounded by a single dural sac.
Progressive neurological lesions may result from the "tethering cord syndrome" (fixation of the spinal cord) by the diastematomyelia phenomenon or any of the associated disorders such as myelodysplasia, dysraphia of the spinal cord.