paraneoplastic pemphigus , PNP (Abkürzung)
pemphigus paraneoplasticus latin

Paraneoplastic pemphigus has been identified in pet dogs.

Paraneoplastic pemphigus, article from eMedicine.

The least common and most severe type of pemphigus is paraneoplastic pemphigus (PNP).

Mutations in this gene are the cause of several cardiomyopathies and keratodermas as well as the autoimmune disease paraneoplastic pemphigus.

Paraneoplastic pemphigus is an autoimmune disorder that is almost invariably linked to an underlying lymphoproliferative disorder.

Additional disorders are sometimes classified as pemphigus including paraneoplastic pemphigus and pemphigus IgA.

Intravenous gamma globulin (IVIG) may be useful in severe cases, especially paraneoplastic pemphigus.

Castleman's is seen in POEMS syndrome and is implicated in 10% of cases of paraneoplastic pemphigus.

There are several types of pemphigus which vary in severity: pemphigus vulgaris, pemphigus foliaceus, Intraepidermal neutrophilic IgA dermatosis, and paraneoplastic pemphigus.